Table 1. List of Lymphoid Neoplasms Recognized by the
International Lymphoma Study Group
B-Cell Neoplasms
I. Precursor B-cell neoplasm: Precursor B lymphoblastic leukemia/
Iymphoma
II. Peripheral B-cell neoplasms
1. B-cell chronic Iymphocytic leukemia/prolymphocytic/
leukemia/small Iymphocytic Iymphoma
2. Lymphoplasmacytoid Iymphoma/ immunocytoma
3. Mantle cell lymphoma
4. Follicle center lymphoma, follicular
Provisional cytologic grades: I (small cell), II (mixed small
and large cell), III (large cell)
Provisional subtype: diffuse, predominantly small cell type
5. Marginal zone B-cell Iymphoma
Extranodal (MALT-type +/- monocytoid B cells)
Provisional subtype: Nodal (+/- monocytoid B cells)
6. Provisional entity: Splenic marginal zone Iymphoma (+/-
villous Iymphocytes)
7. Hairy cell leukemia
8. Plasmacytoma/plasma cell myeloma
9. Diffuse Large B-cell Iymphoma*
Subtype: Primary mediastinal (thymic) B-cell Iymphoma
10. Burkitt's Iymphoma
11. Provisional entity: High-grade B-cell Iymphoma. Burkitt-like*
T-Cell and Putative NK-Cell Neoplasms
I. Precursor T-cell neoplasm: Precursor T-lymphoblastic
Iymphoma/leukemia
II. Peripheral T-cell and NK-cell neoplasms
1. T-cell chronic Iymphocytic leukemia/prolymphocytic
leukemia
2. Large granular Iymphocyte leukemia (LGL)
T-cell type
NK cell type
3. Mycosis fungoides/Sezary syndrome
4. Peripheral T-cell Iymphomas, unspecified*
Provisional cytologic categories: medium-sized cell, mixed
medium and large cell, large cell, Iymphoepithelioid cell
Provisional subtype: Hepatosplenic g/d T-cell Iymphoma
Provisional subtype: Subcutaneous panniculitic T-cell
Iymphoma
5. Angioimmunoblastic T-cell Iymphoma (AILD)
6. Angiocentric Iymphoma
7. Intestinal T-cell Iymphoma (+/- enteropathy associated)
8. Adult T-cell Iymphoma/leukemia (ATL/L)
9. Anaplastic large cell Iymphoma (ALCL). CD30+, T- and null
cell types
10. Provisional entity: Anaplastic large-cell lymphoma.
Hodgkin's-like
Hodgkin's Disease
I. Lymphocyte predominance
II. Nodular sclerosis
III. Mixed cellularity
IV. Lymphocyte depletion
V. Provisional entity: Lymphocyte-rich classical HD
*These categories are thought likely to include more than one disease entity. visional